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{"creatorNames": [{"creatorName": "KODAMA, Hirokazu"}], "nameIdentifiers": [{"nameIdentifier": "887", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "20581929", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=20581929"}]}, {"creatorNames": [{"creatorName": "SHIOMI, Motonori"}], "nameIdentifiers": [{"nameIdentifier": "8220", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "MAEKAWA, Takeru"}], "nameIdentifiers": [{"nameIdentifier": "8218", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "MURAMOTO, Keiji"}], "nameIdentifiers": [{"nameIdentifier": "6906", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "FUKUO, Asuka"}], "nameIdentifiers": [{"nameIdentifier": "8221", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "YAMAGUCHI, Tsuyoshi"}], "nameIdentifiers": [{"nameIdentifier": "627", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "10510290", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=10510290"}]}, {"creatorNames": [{"creatorName": "MORITANI, Suzuko"}], "nameIdentifiers": [{"nameIdentifier": "7460", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "20283559", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=20283559"}]}, {"creatorNames": [{"creatorName": "TANI, Masaji"}], "nameIdentifiers": [{"nameIdentifier": "696", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "60236677", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=60236677"}, {"nameIdentifier": "0000-0003-1270-6003", "nameIdentifierScheme": "ORCID", "nameIdentifierURI": "https://orcid.org/0000-0003-1270-6003"}]}]}, "item_3_description_4": {"attribute_name": "抄録", "attribute_value_mlt": [{"subitem_description": "肝原発の血管筋脂肪腫(angiomyolipoma; AML)は、肝細胞癌と鑑別が困難な場合がある。今回、単発の肝腫瘍に対して肝細胞癌を否定できず切除を行ったが、病理組織学的検査でAMLと診断した一例を経験したので報告する。症例は50歳代の女性。検診にて外側区域の肝腫瘍を指摘され、加療目的に紹介となった。造影CT検査では肝外側区域、門脈臍部に接して2cm大の腫瘍性病変を認め、動脈相で濃染し平衡相でwashoutしていた。腹部MRI検査では同部位にT2強調像で高信号、T1 out of phaseにて若干の信号低下を認めた。Gadolinium-ethoxybenzyl-diethylene-triaminepentaacetic-acid(Gd-EOB-DTPA; EOB) MRIでは動脈相で濃染、門脈相から平衡相にかけてwashoutし、肝細胞相では低信号であった。画像所見から肝細胞癌を疑い、腹腔鏡下肝左葉切除術を施行した。病理組織学的には好酸性紡錘形細胞や淡明~淡好酸性細胞の上皮様配列がみられ、内部に脂肪組織が島状に介在し、また、平滑筋性の厚い壁を持った血管構造も一部存在しており、肝血管筋脂肪腫と診断した。一般に脂肪成分の少ないAMLは、肝細胞癌との鑑別が困難である。最近では、肝静脈への流出血管の有無が鑑別診断に有用であるとの報告が見られるため、これらを注意深く観察すべきと考えられた。", "subitem_description_type": "Abstract"}, {"subitem_description": "Hepatic angiomyolipoma (AML) may be difficult to distinguish from hepatocellular carcinoma. Here we report a resected case of a hepatic AML mimicking hepatocellular carcinoma. The patient was a woman in her 50s referred for further evaluation of a tumor in the left lateral segment of the liver. Contrast-enhanced computed tomography showed a two cm-sized tumor attached with the umbilical portion in the left lateral segment of the liver, which was enhanced in the arterial phase and washed out in the portal venous phase. Abdominal MRI showed a high-intensity tumor on T2-weighted image and a slight decrease of signal intensity on T1 out of phase. The tumor on Gd-EOB-DTPA enhanced MRI displayed high intensity in the arterial phase and washout in the portal venous phase, and low signal intensity in hepatobiliary phase. Based on these imaging findings, we suspected hepatocellular carcinoma and a laparoscopic left lobectomy was performed. Histopathological examination showed spindle and perivascular epithelioid cells and a few fat cells, and immunohistochemical analysis revealed positive staining of HMB-45 and αSMA. The tumor was diagnosed as a hepatic AML. Hepatic AML with a small fatty component is generally difficult to distinguish from hepatocellular carcinoma. More recently, the presence of outflow blood vessels to the hepatic vein has been reported to be useful in the differential diagnosis for AML. These imaging findings should be carefully observed.", "subitem_description_type": "Abstract"}]}, "item_3_description_42": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"subitem_description": "Departmental Bulletin Paper", "subitem_description_type": "Other"}]}, "item_3_identifier_registration": {"attribute_name": "ID登録", "attribute_value_mlt": [{"subitem_identifier_reg_text": "10.14999/1521.00012864", "subitem_identifier_reg_type": "JaLC"}]}, "item_3_publisher_32": {"attribute_name": "出版者", "attribute_value_mlt": [{"subitem_publisher": "滋賀医科大学雑誌編集委員会"}]}, "item_3_relation_11": {"attribute_name": "DOI", "attribute_value_mlt": [{"subitem_relation_name": [{"subitem_relation_name_text": "10.14999/1521.00012864"}], "subitem_relation_type": "isIdenticalTo", "subitem_relation_type_id": {"subitem_relation_type_id_text": "http://doi.org/10.14999/1521.00012864", "subitem_relation_type_select": "DOI"}}]}, "item_3_version_type_15": {"attribute_name": "著者版フラグ", "attribute_value_mlt": [{"subitem_version_resource": "http://purl.org/coar/version/c_970fb48d4fbd8a85", "subitem_version_type": "VoR"}]}, "item_creator": {"attribute_name": "著者", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "萩野, 元晴"}], "nameIdentifiers": [{"nameIdentifier": "8289", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "飯田, 洋也"}], "nameIdentifiers": [{"nameIdentifier": "844", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "30733901", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=30733901"}, {"nameIdentifier": "0000-0001-6245-4583", "nameIdentifierScheme": "ORCID", "nameIdentifierURI": "https://orcid.org/0000-0001-6245-4583"}]}, {"creatorNames": [{"creatorName": "前平, 博充"}], "nameIdentifiers": [{"nameIdentifier": "6759", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "0000-0003-3064-5216", "nameIdentifierScheme": "ORCID", "nameIdentifierURI": 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"徳田, 彩"}], "nameIdentifiers": [{"nameIdentifier": "6933", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "80814392", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=80814392"}]}, {"creatorNames": [{"creatorName": "三宅, 亨"}], "nameIdentifiers": [{"nameIdentifier": "812", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "70581924", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=70581924"}]}, {"creatorNames": [{"creatorName": "植木, 智之"}], "nameIdentifiers": [{"nameIdentifier": "811", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "0000-0002-7285-5222", "nameIdentifierScheme": "ORCID", "nameIdentifierURI": "https://orcid.org/0000-0002-7285-5222"}]}, {"creatorNames": [{"creatorName": "小島, 正継"}], "nameIdentifiers": [{"nameIdentifier": "3245", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "10452236", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=10452236"}]}, {"creatorNames": [{"creatorName": "児玉, 泰一"}], "nameIdentifiers": [{"nameIdentifier": "887", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "20581929", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=20581929"}]}, {"creatorNames": [{"creatorName": "塩見, 一徳"}], "nameIdentifiers": [{"nameIdentifier": "8220", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "前川, 毅"}], "nameIdentifiers": [{"nameIdentifier": "8218", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "村本, 圭史"}], "nameIdentifiers": [{"nameIdentifier": "6906", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "福尾, 飛翔"}], "nameIdentifiers": [{"nameIdentifier": "8221", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "山口, 剛"}], "nameIdentifiers": [{"nameIdentifier": "627", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "10510290", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=10510290"}]}, {"creatorNames": [{"creatorName": "森谷, 鈴子"}], "nameIdentifiers": [{"nameIdentifier": "7460", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "20283559", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=20283559"}]}, {"creatorNames": [{"creatorName": "谷, 眞至"}], "nameIdentifiers": [{"nameIdentifier": "696", "nameIdentifierScheme": "WEKO"}, {"nameIdentifier": "60236677", "nameIdentifierScheme": "e-Rad", "nameIdentifierURI": "https://kaken.nii.ac.jp/ja/search/?qm=60236677"}, {"nameIdentifier": "0000-0003-1270-6003", "nameIdentifierScheme": "ORCID", "nameIdentifierURI": "https://orcid.org/0000-0003-1270-6003"}]}]}, "item_files": {"attribute_name": "ファイル情報", "attribute_type": "file", "attribute_value_mlt": [{"accessrole": "open_date", "date": [{"dateType": "Available", "dateValue": "2020-12-01"}], "displaytype": "detail", "download_preview_message": "", "file_order": 0, "filename": "jsums3401p005.pdf", "filesize": [{"value": "1.4 MB"}], "format": "application/pdf", "future_date_message": "", "is_thumbnail": false, "licensetype": "license_free", "mimetype": "application/pdf", "size": 1400000.0, "url": {"label": "jsums3401p005", "url": "https://shiga-med.repo.nii.ac.jp/record/3754/files/jsums3401p005.pdf"}, "version_id": "2f150c37-2cae-41ce-80e7-aaa2f92f763f"}]}, "item_keyword": {"attribute_name": "キーワード", "attribute_value_mlt": [{"subitem_subject": "肝血管筋脂肪腫", "subitem_subject_scheme": "Other"}, {"subitem_subject": "肝細胞癌", "subitem_subject_scheme": "Other"}, {"subitem_subject": "流出静脈", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Angiomyolipoma", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}, {"subitem_subject": "hepatocellular carcinoma", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}, {"subitem_subject": "drainage vein", "subitem_subject_language": "en", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "言語", "attribute_value_mlt": [{"subitem_language": "jpn"}]}, "item_resource_type": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"resourcetype": "departmental bulletin paper", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "肝細胞癌と鑑別が困難であった肝血管筋脂肪腫の1例", "item_titles": {"attribute_name": "タイトル", "attribute_value_mlt": [{"subitem_title": "肝細胞癌と鑑別が困難であった肝血管筋脂肪腫の1例"}, {"subitem_title": "A Case of Hepatic Angiomyolipoma Mimicking Hepatocellular Carcinoma.", "subitem_title_language": "en"}]}, "item_type_id": "3", "owner": "11", "path": ["372"], "permalink_uri": "https://doi.org/10.14999/1521.00012864", "pubdate": {"attribute_name": "公開日", "attribute_value": "2020-12-01"}, "publish_date": "2020-12-01", "publish_status": "0", "recid": "3754", "relation": {}, "relation_version_is_last": true, "title": ["肝細胞癌と鑑別が困難であった肝血管筋脂肪腫の1例"], "weko_shared_id": -1}
  1. 紀要
  2. 滋賀医科大学雑誌
  3. 第34巻, 2021
  4. 第1号(医学編)

肝細胞癌と鑑別が困難であった肝血管筋脂肪腫の1例

https://doi.org/10.14999/1521.00012864
https://doi.org/10.14999/1521.00012864
07c77375-06c1-4ef9-b23e-5d85da6ef1b0
名前 / ファイル ライセンス アクション
jsums3401p005.pdf jsums3401p005 (1.4 MB)
Item type 紀要論文 / Departmental Bulletin Paper(1)
公開日 2020-12-01
タイトル
タイトル 肝細胞癌と鑑別が困難であった肝血管筋脂肪腫の1例
タイトル
言語 en
タイトル A Case of Hepatic Angiomyolipoma Mimicking Hepatocellular Carcinoma.
言語
言語 jpn
キーワード
主題Scheme Other
主題 肝血管筋脂肪腫
キーワード
主題Scheme Other
主題 肝細胞癌
キーワード
主題Scheme Other
主題 流出静脈
キーワード
言語 en
主題Scheme Other
主題 Angiomyolipoma
キーワード
言語 en
主題Scheme Other
主題 hepatocellular carcinoma
キーワード
言語 en
主題Scheme Other
主題 drainage vein
資源タイプ
資源タイプ識別子 http://purl.org/coar/resource_type/c_6501
資源タイプ departmental bulletin paper
ID登録
ID登録 10.14999/1521.00012864
ID登録タイプ JaLC
タイトル(ヨミ)
その他のタイトル カンサイボウガン ト カンベツ ガ コンナンデアッタ カンケッカンキン シボウシュ ノ 1レイ
著者 萩野, 元晴

× 萩野, 元晴

WEKO 8289

萩野, 元晴

Search repository
飯田, 洋也

× 飯田, 洋也

WEKO 844
e-Rad 30733901
ORCID 0000-0001-6245-4583

飯田, 洋也

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前平, 博充

× 前平, 博充

WEKO 6759
ORCID 0000-0003-3064-5216

前平, 博充

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森, 治樹

× 森, 治樹

WEKO 6959
e-Rad 40803945

森, 治樹

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貝田, 佐知子

× 貝田, 佐知子

WEKO 629
e-Rad 70710234
ORCID 0000-0002-1279-5942

貝田, 佐知子

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石川, 健

× 石川, 健

WEKO 8222

石川, 健

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竹林, 克士

× 竹林, 克士

WEKO 3247

竹林, 克士

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徳田, 彩

× 徳田, 彩

WEKO 6933
e-Rad 80814392

徳田, 彩

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三宅, 亨

× 三宅, 亨

WEKO 812
e-Rad 70581924

三宅, 亨

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植木, 智之

× 植木, 智之

WEKO 811
ORCID 0000-0002-7285-5222

植木, 智之

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小島, 正継

× 小島, 正継

WEKO 3245
e-Rad 10452236

小島, 正継

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児玉, 泰一

× 児玉, 泰一

WEKO 887
e-Rad 20581929

児玉, 泰一

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塩見, 一徳

× 塩見, 一徳

WEKO 8220

塩見, 一徳

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前川, 毅

× 前川, 毅

WEKO 8218

前川, 毅

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村本, 圭史

× 村本, 圭史

WEKO 6906

村本, 圭史

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福尾, 飛翔

× 福尾, 飛翔

WEKO 8221

福尾, 飛翔

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山口, 剛

× 山口, 剛

WEKO 627
e-Rad 10510290

山口, 剛

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森谷, 鈴子

× 森谷, 鈴子

WEKO 7460
e-Rad 20283559

森谷, 鈴子

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谷, 眞至

× 谷, 眞至

WEKO 696
e-Rad 60236677
ORCID 0000-0003-1270-6003

谷, 眞至

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著者別名 HAGINO, Motoharu

× HAGINO, Motoharu

WEKO 8289

HAGINO, Motoharu

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IIDA, Hiroya

× IIDA, Hiroya

WEKO 844
e-Rad 30733901
ORCID 0000-0001-6245-4583

IIDA, Hiroya

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MAEHIRA, Hiromitsu

× MAEHIRA, Hiromitsu

WEKO 6759
ORCID 0000-0003-3064-5216

MAEHIRA, Hiromitsu

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MORI, Haruki

× MORI, Haruki

WEKO 6959
e-Rad 40803945

MORI, Haruki

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KAIDA, Sachiko

× KAIDA, Sachiko

WEKO 629
e-Rad 70710234
ORCID 0000-0002-1279-5942

KAIDA, Sachiko

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内容記述タイプ Abstract
内容記述 肝原発の血管筋脂肪腫(angiomyolipoma; AML)は、肝細胞癌と鑑別が困難な場合がある。今回、単発の肝腫瘍に対して肝細胞癌を否定できず切除を行ったが、病理組織学的検査でAMLと診断した一例を経験したので報告する。症例は50歳代の女性。検診にて外側区域の肝腫瘍を指摘され、加療目的に紹介となった。造影CT検査では肝外側区域、門脈臍部に接して2cm大の腫瘍性病変を認め、動脈相で濃染し平衡相でwashoutしていた。腹部MRI検査では同部位にT2強調像で高信号、T1 out of phaseにて若干の信号低下を認めた。Gadolinium-ethoxybenzyl-diethylene-triaminepentaacetic-acid(Gd-EOB-DTPA; EOB) MRIでは動脈相で濃染、門脈相から平衡相にかけてwashoutし、肝細胞相では低信号であった。画像所見から肝細胞癌を疑い、腹腔鏡下肝左葉切除術を施行した。病理組織学的には好酸性紡錘形細胞や淡明~淡好酸性細胞の上皮様配列がみられ、内部に脂肪組織が島状に介在し、また、平滑筋性の厚い壁を持った血管構造も一部存在しており、肝血管筋脂肪腫と診断した。一般に脂肪成分の少ないAMLは、肝細胞癌との鑑別が困難である。最近では、肝静脈への流出血管の有無が鑑別診断に有用であるとの報告が見られるため、これらを注意深く観察すべきと考えられた。
抄録
内容記述タイプ Abstract
内容記述 Hepatic angiomyolipoma (AML) may be difficult to distinguish from hepatocellular carcinoma. Here we report a resected case of a hepatic AML mimicking hepatocellular carcinoma. The patient was a woman in her 50s referred for further evaluation of a tumor in the left lateral segment of the liver. Contrast-enhanced computed tomography showed a two cm-sized tumor attached with the umbilical portion in the left lateral segment of the liver, which was enhanced in the arterial phase and washed out in the portal venous phase. Abdominal MRI showed a high-intensity tumor on T2-weighted image and a slight decrease of signal intensity on T1 out of phase. The tumor on Gd-EOB-DTPA enhanced MRI displayed high intensity in the arterial phase and washout in the portal venous phase, and low signal intensity in hepatobiliary phase. Based on these imaging findings, we suspected hepatocellular carcinoma and a laparoscopic left lobectomy was performed. Histopathological examination showed spindle and perivascular epithelioid cells and a few fat cells, and immunohistochemical analysis revealed positive staining of HMB-45 and αSMA. The tumor was diagnosed as a hepatic AML. Hepatic AML with a small fatty component is generally difficult to distinguish from hepatocellular carcinoma. More recently, the presence of outflow blood vessels to the hepatic vein has been reported to be useful in the differential diagnosis for AML. These imaging findings should be carefully observed.
書誌情報 滋賀医科大学雑誌

巻 34, 号 1, p. 5-9, 発行日 2020-11-30
出版者
出版者 滋賀医科大学雑誌編集委員会
DOI
関連タイプ isIdenticalTo
識別子タイプ DOI
関連識別子 http://doi.org/10.14999/1521.00012864
関連名称 10.14999/1521.00012864
著者版フラグ
出版タイプ VoR
出版タイプResource http://purl.org/coar/version/c_970fb48d4fbd8a85
資源タイプ
内容記述タイプ Other
内容記述 Departmental Bulletin Paper
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