{"created":"2023-06-19T10:44:00.368998+00:00","id":4372,"links":{},"metadata":{"_buckets":{"deposit":"26d01ad8-1f5e-4823-b53f-df15a181d960"},"_deposit":{"created_by":11,"id":"4372","owners":[11],"pid":{"revision_id":0,"type":"depid","value":"4372"},"status":"published"},"_oai":{"id":"oai:shiga-med.repo.nii.ac.jp:00004372","sets":["30:46:84","30:59:221"]},"author_link":["1869","7867","1939","6817","9181","2797","2710","2814","538","7807","1890"],"item_4_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2022-10-15","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"20","bibliographicPageEnd":"3081","bibliographicPageStart":"3077","bibliographicVolumeNumber":"61","bibliographic_titles":[{},{"bibliographic_title":"Internal medicine (Tokyo, Japan)","bibliographic_titleLang":"en"}]}]},"item_4_creator_3":{"attribute_name":"著者別名","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"久米, 真司"}],"nameIdentifiers":[{"nameIdentifier":"1869","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00452235","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00452235"},{"nameIdentifier":"0000-0001-6937-9715","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0001-6937-9715"}]},{"creatorNames":[{"creatorName":"山原, 真子"}],"nameIdentifiers":[{"nameIdentifier":"7807","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"70731941","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=70731941"}]},{"creatorNames":[{"creatorName":"上原, 孔美"}],"nameIdentifiers":[{"nameIdentifier":"9181","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"桑形, 尚吾"}],"nameIdentifiers":[{"nameIdentifier":"6817","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00791617","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00791617"}]},{"creatorNames":[{"creatorName":"山原, 康佑"}],"nameIdentifiers":[{"nameIdentifier":"2797","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"50731915","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=50731915"}]},{"creatorNames":[{"creatorName":"武田, 尚子"}],"nameIdentifiers":[{"nameIdentifier":"2710","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"20737655","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=20737655"}]},{"creatorNames":[{"creatorName":"金崎, 雅美"}],"nameIdentifiers":[{"nameIdentifier":"1890","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"30402720","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=30402720"}]},{"creatorNames":[{"creatorName":"加藤, 浩一"}],"nameIdentifiers":[{"nameIdentifier":"2814","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"70736983","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=70736983"},{"nameIdentifier":"0000-0002-6125-0789","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0002-6125-0789"}]},{"creatorNames":[{"creatorName":"大野, 聖子"}],"nameIdentifiers":[{"nameIdentifier":"1939","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"20610025","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=20610025"},{"nameIdentifier":"0000-0003-1209-8896","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0003-1209-8896"}]},{"creatorNames":[{"creatorName":"中川, 義久"}],"nameIdentifiers":[{"nameIdentifier":"7867","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00378613","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00378613"}]},{"creatorNames":[{"creatorName":"前川, 聡"}],"nameIdentifiers":[{"nameIdentifier":"538","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00209363","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00209363"},{"nameIdentifier":"0000-0002-4611-8149","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0002-4611-8149"}]}]},"item_4_description_14":{"attribute_name":"フォーマット","attribute_value_mlt":[{"subitem_description":"application/pdf","subitem_description_type":"Other"}]},"item_4_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Fabry disease is an inherited lysosomal disorder caused by mutations in the alpha-galactosidase A gene. We herein report a Fabry disease patient with enzyme replacement therapy (ERT)-resistant proteinuria who showed improvement in the estimated glomerular filtration rate (eGFR) decline rate after uric acid (UA)-lowering therapy. The patient was diagnosed with Fabry disease at 36 years old. After that, even under ERT, proteinuria and eGFR decline persisted. During the clinical course, serum UA levels were elevated with increases in renal tubular damage markers. Febuxostat administration immediately improved tubular damage and prevented further eGFR decline. UA-mediated tubulopathy may become an additional therapeutic target for eGFR decline in Fabry disease.","subitem_description_type":"Abstract"}]},"item_4_description_42":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"subitem_description":"Journal Article","subitem_description_type":"Other"}]},"item_4_publisher_32":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"The Japanese Society of Internal Medicine"}]},"item_4_publisher_34":{"attribute_name":"別言語の出版者","attribute_value_mlt":[{"subitem_publisher":"日本内科学会"}]},"item_4_relation_10":{"attribute_name":"PubMed番号","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"35283375","subitem_relation_type_select":"PMID"}}]},"item_4_relation_11":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_name":[{"subitem_relation_name_text":"10.2169/internalmedicine.8993-21"}],"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.2169/internalmedicine.8993-21","subitem_relation_type_select":"DOI"}}]},"item_4_rights_12":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"Ⓒ 2022 The Japanese Society of Internal Medicine"}]},"item_4_source_id_7":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"1349-7235","subitem_source_identifier_type":"ISSN"}]},"item_4_version_type_15":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"KUME, Shinji"}],"nameIdentifiers":[{"nameIdentifier":"1869","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00452235","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00452235"},{"nameIdentifier":"0000-0001-6937-9715","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0001-6937-9715"}]},{"creatorNames":[{"creatorName":"YASUDA-YAMAHARA, Mako"}],"nameIdentifiers":[{"nameIdentifier":"7807","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"70731941","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=70731941"}]},{"creatorNames":[{"creatorName":"IMAMURA-UEHARA, Yoshimi"}],"nameIdentifiers":[{"nameIdentifier":"9181","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"KUWAGATA, Shogo"}],"nameIdentifiers":[{"nameIdentifier":"6817","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00791617","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00791617"}]},{"creatorNames":[{"creatorName":"YAMAHARA, Kosuke"}],"nameIdentifiers":[{"nameIdentifier":"2797","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"50731915","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=50731915"}]},{"creatorNames":[{"creatorName":"TAKEDA, Naoko"}],"nameIdentifiers":[{"nameIdentifier":"2710","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"20737655","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=20737655"}]},{"creatorNames":[{"creatorName":"CHIN-KANASAKI, Masami"}],"nameIdentifiers":[{"nameIdentifier":"1890","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"30402720","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=30402720"}]},{"creatorNames":[{"creatorName":"KATO, Koichi"}],"nameIdentifiers":[{"nameIdentifier":"2814","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"70736983","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=70736983"},{"nameIdentifier":"0000-0002-6125-0789","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0002-6125-0789"}]},{"creatorNames":[{"creatorName":"OHNO, Seiko"}],"nameIdentifiers":[{"nameIdentifier":"1939","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"20610025","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=20610025"},{"nameIdentifier":"0000-0003-1209-8896","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0003-1209-8896"}]},{"creatorNames":[{"creatorName":"NAKAGAWA, Yoshihisa"}],"nameIdentifiers":[{"nameIdentifier":"7867","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00378613","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00378613"}]},{"creatorNames":[{"creatorName":"MAEGAWA, Hiroshi"}],"nameIdentifiers":[{"nameIdentifier":"538","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"00209363","nameIdentifierScheme":"e-Rad","nameIdentifierURI":"https://kaken.nii.ac.jp/ja/search/?qm=00209363"},{"nameIdentifier":"0000-0002-4611-8149","nameIdentifierScheme":"ORCID","nameIdentifierURI":"https://orcid.org/0000-0002-4611-8149"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2022-11-10"}],"displaytype":"detail","filename":"internalmedicine.8993-21.pdf","filesize":[{"value":"592.4 kB"}],"format":"application/pdf","license_note":"The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"internalmedicine.8993-21","url":"https://shiga-med.repo.nii.ac.jp/record/4372/files/internalmedicine.8993-21.pdf"},"version_id":"65eb32c9-5ae0-4b01-8b5a-32770e79487d"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Fabry disease","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"hyperuricemia","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"tubular cell damage","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"xanthine oxidase inhibitor","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"urate crystal","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Improvement in Decline Rate of Estimated Glomerular Filtration Rate after Febuxostat Treatment in a Fabry Disease Patient with Enzyme Replacement Therapy-resistant Proteinuria.","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Improvement in Decline Rate of Estimated Glomerular Filtration Rate after Febuxostat Treatment in a Fabry Disease Patient with Enzyme Replacement Therapy-resistant Proteinuria."}]},"item_type_id":"4","owner":"11","path":["84","221"],"pubdate":{"attribute_name":"公開日","attribute_value":"2022-11-10"},"publish_date":"2022-11-10","publish_status":"0","recid":"4372","relation_version_is_last":true,"title":["Improvement in Decline Rate of Estimated Glomerular Filtration Rate after Febuxostat Treatment in a Fabry Disease Patient with Enzyme Replacement Therapy-resistant Proteinuria."],"weko_creator_id":"11","weko_shared_id":-1},"updated":"2023-06-19T11:09:49.989134+00:00"}