{"created":"2023-06-19T10:43:40.090148+00:00","id":3933,"links":{},"metadata":{"_buckets":{"deposit":"40c05b11-c308-4cee-bd90-7a15126d77e7"},"_deposit":{"created_by":11,"id":"3933","owners":[11],"pid":{"revision_id":0,"type":"depid","value":"3933"},"status":"published"},"_oai":{"id":"oai:shiga-med.repo.nii.ac.jp:00003933","sets":["30:198:199"]},"author_link":["2836","552","7986","3015","8553","8552","8494","2501","8493","1956"],"item_4_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2021-06-15","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"12","bibliographicPageEnd":"1939","bibliographicPageStart":"1935","bibliographicVolumeNumber":"60","bibliographic_titles":[{},{"bibliographic_title":"Internal medicine (Tokyo, Japan)","bibliographic_titleLang":"en"}]}]},"item_4_creator_3":{"attribute_name":"著者別名","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"中村, 竜太郎"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"北村, 彰浩"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"塚本, 剛士"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"音羽, 祐兵"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"岡本, 直己"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"小川, 暢弘"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"山川, 勇"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"金, 一暁"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"真田, 充"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"漆谷, 真"}],"nameIdentifiers":[{},{},{}]}]},"item_4_description_14":{"attribute_name":"フォーマット","attribute_value_mlt":[{"subitem_description":"pdf","subitem_description_type":"Other"}]},"item_4_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"A 23-year-old woman was admitted for slowly progressive proximal limb muscle weakness from childhood with elevated muscle enzyme levels. Although muscular diseases were suspected, an electromyogram showed remarkable neurogenic changes, and a muscle echogram indicated selective muscle involvement, including dissociation between the soleus and gastrocnemius, which was consistent with previous reports using magnetic resonance imaging (MRI). She was diagnosed with SMA type 3 following genetic testing, and nusinersen was soon initiated. An early diagnosis is mandatory to maximize the benefit of treatment. A muscle echogram may facilitate an early diagnosis in a non-invasive and time-saving manner compared to MRI.","subitem_description_type":"Abstract"}]},"item_4_description_42":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"subitem_description":"Journal Article","subitem_description_type":"Other"}]},"item_4_publisher_32":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"Japanese Society of Internal Medicine"}]},"item_4_publisher_34":{"attribute_name":"別言語の出版者","attribute_value_mlt":[{"subitem_publisher":"日本内科学会"}]},"item_4_relation_10":{"attribute_name":"PubMed番号","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"33456041","subitem_relation_type_select":"PMID"}}]},"item_4_relation_11":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_name":[{"subitem_relation_name_text":"10.2169/internalmedicine.6396-20"}],"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.2169/internalmedicine.6396-20","subitem_relation_type_select":"DOI"}}]},"item_4_rights_12":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"© 2021 by The Japanese Society of Internal Medicine"}]},"item_4_source_id_7":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"1349-7235","subitem_source_identifier_type":"ISSN"}]},"item_4_version_type_15":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"NAKAMURA, Ryutaro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KITAMURA, Akihiro"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"TSUKAMOTO, Takahito"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OTOWA, Yuhei"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OKAMOTO, Naoki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"OGAWA, Nobuhiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"YAMAKAWA, Isamu"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"KIM, Hyoh"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"SANADA, Mitsuru"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"URUSHITANI, Makoto"}],"nameIdentifiers":[{},{},{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2021-06-29"}],"displaytype":"detail","filename":"internalmedicine.6396-20.pdf","filesize":[{"value":"3.7 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"internalmedicine.6396-20","url":"https://shiga-med.repo.nii.ac.jp/record/3933/files/internalmedicine.6396-20.pdf"},"version_id":"28ae17ca-b719-4902-8853-1b1d3a1b7bdc"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"SMA","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"luminosity ratio","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"muscle MRI","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"muscle ultrasound","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"nusinersen","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"selective muscle involvement","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Spinal Muscular Atrophy Type 3 Showing a Specific Pattern of Selective Vulnerability on Muscle Ultrasound.","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Spinal Muscular Atrophy Type 3 Showing a Specific Pattern of Selective Vulnerability on Muscle Ultrasound."}]},"item_type_id":"4","owner":"11","path":["199"],"pubdate":{"attribute_name":"公開日","attribute_value":"2021-06-29"},"publish_date":"2021-06-29","publish_status":"0","recid":"3933","relation_version_is_last":true,"title":["Spinal Muscular Atrophy Type 3 Showing a Specific Pattern of Selective Vulnerability on Muscle Ultrasound."],"weko_creator_id":"11","weko_shared_id":-1},"updated":"2023-06-19T11:25:27.989618+00:00"}